Recommended in the Brandon/Hill selected list of print books and journals for the small medical library - April 2003 This is the definitive book on pediatric liver disease, providing extensive, well-edited information that is not easily accessible or available in other textbooks. The book contains comprehensive information that explains the pathophysiology, clinical and laboratory diagnosis and clinical manifestations of liver disease. This is a "must have" for those interested in this rapidly growing pediatric subspeciality
Table of Contents
Part 1 Pathophysiology of paediatric liver disease: structural and functional development of the liver; mechanisms and morphology of cholestasis; the cholangiopathies; fulminant hepatic failure in children; portal hypertension. Part 2 Evaluation of liver disease: laboratory assessment of liver function and injury in children; laboratory diagnosis of inborn errors of metabolism. Part 3 Cholestatic liver diseases: approach to the infant with cholestasis; medical and nutritional management of cholestasis; neonatal hepatitis and congenital infections; biliary atresia and other disorders of the extrahepatic bile ducts; neonatal jaundice and disorders of bilirubin metabolism, familial hepatocellular cholestasis; Alagille syndrome; diseases of the gallbladder in infancy, childhood, and adolescence. Part 4 Hepatitis and immune disorders: acute and chronic viral hepatitis; autoimmune hepatitis; sclerosing cholangitis; drug-induced liver disease; immune deficiency and the liver. Part 5 Metabolic liver disease: approach to child with metabolic liver disease; alpha1-antitrypsin deficiency; the liver and biliary tract in cystic fibrosis; inborn errors of carbohydrate metabolism; copper and iron storage disorders; neonatal haemochromatosis; porphyrins and porphyria; tyrosinemia; the lysosomal storage disorders; inborn errors of bile acid metabolism; inborn defects in mitochondrial fatty acid oxidation; mitochondrial hepatopathies; perioxisomal diseases; disorders of the urea cycle. Part 6 Other conditions and issues in paediatric hepatology: bacterial, parasitic, and fungal infections of the liver; systemic disease and the liver; fibrocystic liver disease; hepatic tumours in children; liver transplantation in children.